Objective: To investigate the clinical features of cystic hepatic lymphangioma and its diagnosis and treatment methods, so as to improve the diagnostic rate and therapeutic efficacy. Methods: The clinical data as well as diagnosis and treatment process of two adult patients with cystic hepatic lymphangioma in Affiliated Hospital of Guangdong Medical University were retrospectively analyzed. The literature on cystic hepatic lymphangioma in periodical databases was retrieved and reviewed. Results: Both patients treated by the authors were female, and were diagnosed as cystic space occupying lesion of the liver and hepatic cyst on admission respectively; then both patients received surgical treatment after completion of the relevant examinations, and were finally diagnosed as cystic hepatic lymphangioma by postoperative pathology; no recurrence occurred in either of them during follow-up and the treatment results were satisfactory. A total of 6 patients with cystic hepatic lymphangioma were reported in China from 1984 to 2017, of whom, 4 cases were male and 2 cases were female; two cases were diagnosed as hepatic cystic lymphangioma (2/6) and all the others (4/6) were misdiagnosed at admission. After surgical resection, the diagnosis was confirmed to be cystic hepatic lymphangioma in all of the 6 cases and they all recovered satisfactorily after operation. Conclusion: Cystic hepatic lymphangioma is a rare benign liver disease, which has no specific clinical symptoms, signs and imaging characteristics, and is likely to be misdiagnosed as liver cysts and other cystic diseases of the liver in clinical practice. MRI can help in differential diagnosis. Treatment plan should be based on the individual conditions of the patients with definite symptoms and signs or if malignancy cannot be excluded. Pathological examination is the only way to make the definite diagnosis.